Endocrine Abstracts

Erdheim Chester disease (ECD) is a non langheransian rare histiocytosis, with around 500 cases described worldwide since its discovery for the first time in 1930 by Jakob Erdheim et William Chester. It is a multivisceral disease, characterized by a proliferation of abnormal histocytes CD68 positive and CD1a negative, including a retroperitoneal and perirenal fibrosis, a peri-aortitis, an osteosclerosis of the lower limbs and sometime an exophthalmia or an diabetes insipidus. H...